KLIPPEL-TRENAUNAY SYNDROM IN FIRST AID DOCTOR’S MEDICAL PRACTCE
https://doi.org/10.25207/1608-6228-2018-25-2-183-186
Abstract
Aim. To acquaint practical health care doctors with clinical display, modern diagnostic methods and treatment techniques of patients with uncommon genetically determined vascular disease, mainly affecting lower limbs vessels – KlippelTrenaunay syndrome.
Materials and methods. The retrospective analyses of anamnesis data, clinical course, laboratory results and instrumental research methods are made, treatment techniques of patients are determined.
Results. Klippel-Trenaunay syndrome is a form of systemic genetic phleboangiosis. Anomaly is diagnosed at birth based on clinical symptoms or infant development, when typical symptoms of diseases are visible. Promptly made instrumental research helps to estimate affection severity of bloodstream, to specify concomitant anomaly in order to choose the most effective treatment method (conservative or surgical).
Conclusion. Knowledge of clinical display, differential diagnostics and prompt treatment techniques for patients with Klippel-Trenaunay syndrome are performed, these data are important for all levels of medical aid to save life quality.
About the Authors
A. S. Bagdasaryan
Federal State Budgetary Educational Institution of Higher Education Kuban State Medical University of the Ministry of Healthcare of the Russian Federation
Russian Federation
Russian Federation
Аrshak S. Bagdasaryan
4, Sedina str., Krasnodar, Russia, 350063
A. A. Sirunyants
Federal State Budgetary Educational Institution of Higher Education Kuban State Medical University of the Ministry of Healthcare of the Russian Federation
Russian Federation
4, Sedina str., Krasnodar, Russia, 350063
Russian Federation
4, Sedina str., Krasnodar, Russia, 350063
M. B. Andreeva
Federal State Budgetary Educational Institution of Higher Education Kuban State Medical University of the Ministry of Healthcare of the Russian Federation
Russian Federation
4, Sedina str., Krasnodar, Russia, 350063
Russian Federation
4, Sedina str., Krasnodar, Russia, 350063
A. I. Remizova
Federal State Budgetary Educational Institution of Higher Education Kuban State Medical University of the Ministry of Healthcare of the Russian Federation
Russian Federation
4, Sedina str., Krasnodar, Russia, 350063
Russian Federation
4, Sedina str., Krasnodar, Russia, 350063
D. V. Pukhnyak
Federal State Budgetary Educational Institution of Higher Education Kuban State Medical University of the Ministry of Healthcare of the Russian Federation
Russian Federation
4, Sedina str., Krasnodar, Russia, 350063
Russian Federation
4, Sedina str., Krasnodar, Russia, 350063
Zh. A. Kamalyan
Local Budgetary Institution of Healthcare Krasnodar Clinical Emergency Hospital
Russian Federation
14, 40 let Pobedi-str., Krasnodar, Russia, 350042
Russian Federation
14, 40 let Pobedi-str., Krasnodar, Russia, 350042
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Review
For citations:
Bagdasaryan A.S., Sirunyants A.A., Andreeva M.B., Remizova A.I., Pukhnyak D.V., Kamalyan Zh.A. KLIPPEL-TRENAUNAY SYNDROM IN FIRST AID DOCTOR’S MEDICAL PRACTCE. Kuban Scientific Medical Bulletin. 2018;25(2):183-186. (In Russ.) https://doi.org/10.25207/1608-6228-2018-25-2-183-186
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